Primary pleuro-pulmonary synovial sarcoma (PPSS) is a rare tumour and poses a diagnostic challenge particularly when unusual histological features are present. We report a case of a 30-year-old immunocompromised human immunodeficiency virus (HIV) sero-positive male who was referred to us with complaints of cough, breathlessness and left-sided chest pain for the past two months. The PPSS can be confirmed on tru-cut biopsy.
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