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VOLUME 56 , ISSUE 4 ( October-December, 2014 ) > List of Articles

CASE REPORT

Pulmonary Capillary Haemangiomatosis: A Rare Cause of Pulmonary Hypertension

K. Anand Babu, K. Supraja

Keywords : Pulmonary capillary haemangiomatosis, Pulmonary hypertension

Citation Information : Babu KA, Supraja K. Pulmonary Capillary Haemangiomatosis: A Rare Cause of Pulmonary Hypertension. Indian J Chest Dis Allied Sci 2014; 56 (4):259-262.

DOI: 10.5005/ijcdas-56-4-259

License: CC BY-NC 4.0

Published Online: 28-06-2022

Copyright Statement:  Copyright © 2014; The Author(s).


Abstract

Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy.

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