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VOLUME 58 , ISSUE 4 ( October-December, 2016 ) > List of Articles


Systemic Sclerosis Sine Scleroderma: A Rare Entity

Aashish Kumar Singh, Nalin Joshi

Keywords : Systemic Sclerosis, Raynaud's phenomenon, Lung

Citation Information : Singh AK, Joshi N. Systemic Sclerosis Sine Scleroderma: A Rare Entity. Indian J Chest Dis Allied Sci 2016; 58 (4):265-268.

DOI: 10.5005/ijcdas-58-4-265

License: CC BY-NC 4.0

Published Online: 18-11-2022

Copyright Statement:  Copyright © 2016; The Author(s).


Systemic sclerosis sine scleroderma is a rare form of limited systemic sclerosis, but without skin involvement. It does not differ in its clinical or laboratory features and prognosis from classical systemic sclerosis. In the absence of cutaneous signs/symptoms, its diagnosis is delayed leading to significant morbidity and mortality. We report the case of a 28-year-old male who presented with dyspnoea on exertion and Raynaud's phenomenon. Diagnostic evaluation confirmed systemic sclerosis sine scleroderma and pulmonary artery hypertension.

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