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VOLUME 64 , ISSUE 4 ( October-December, 2022 ) > List of Articles


Pulmonary Capillary Hemangiomatosis without Pulmonary Arterial Hypertension Mimicking Interstitial Lung Disease

Vishnu Gopalakrishnan, Akhilesh Kunoor, Jyothi Sreekanth, Malini Eapen, KR Balasubramoniam

Keywords : Interstitial lung disease, Lung biopsy, Pulmonary capillary hemangiomatosis, Pulmonary arterial hypertension

Citation Information : Gopalakrishnan V, Kunoor A, Sreekanth J, Eapen M, Balasubramoniam K. Pulmonary Capillary Hemangiomatosis without Pulmonary Arterial Hypertension Mimicking Interstitial Lung Disease. Indian J Chest Dis Allied Sci 2022; 64 (4):269-271.

DOI: 10.5005/jp-journals-11007-0029

License: CC BY-NC 4.0

Published Online: 05-01-2023

Copyright Statement:  Copyright © 2022; The Author(s).


Pulmonary capillary hemangiomatosis (PCH) is a rare disease usually associated with pulmonary hypertension which is classified in group I as per the World Health Organization (WHO) classification of pulmonary arterial hypertension (PAH). It is commonly presented as effort intolerance and hypoxia. Pulmonary capillary hemangiomatosis can present with ground-glass opacity on chest radiograph which can mimic interstitial lung disease. We need to consider PCH also in the differential diagnosis of interstitial shadows with these clinical presentations and should consider diagnostic evaluation for the same in case of unsatisfactory clinic-radiological response to treatment. We describe a case presented and treated as interstitial lung disease, which turned out to be PCH on lung biopsy. Interestingly, the case was not associated with any evidence of PAH.

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