Citation Information :
Rai DK, Gupta VB, Sharma P, Harish A, Mohanta PC. Takayasu Arteritis in a Young Male: A Rare Entity with an Unusual Presentation. Indian J Chest Dis Allied Sci 2023; 65 (2):92-95.
Takayasu arteritis (TA) is a large vessel pan arteritis of an unknown etiology with a strong female predominance and is seen in the age group of 25–30 years. It presents with non-specific symptoms. Our patient was a young male who presented to us with massive hemoptysis. Fiberoptic bronchoscopy was performed, clots were retrieved, and hemostasis was achieved. Computed tomography pulmonary angiography (CTPA) was done as a part of the workup which revealed dilated and tortuous bronchial arteries along with concentric thickening of the thoracic and abdominal aorta and its branches. A diagnosis of TA was kept in mind and further workup was initiated. The patient had multiple non-specific symptoms which he initially ignored but they helped to clinch the diagnosis. He had a clinically active disease (according to the Indian Takayasu Activity Score), hence initiated on corticosteroid therapy. The patient had symptomatic improvement with no further episodes of hemoptysis and is doing well on follow-up. This case highlights the importance of a meticulous workup in a case of massive hemoptysis as it can be the earliest worrisome symptom for the patient which brings him to the respiratory physician. Also, one should think of this disease entity even in a young male.
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