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VOLUME 64 , ISSUE 2 ( April-June, 2022 ) > List of Articles


Unilateral Presentation of Pulmonary Alveolar Proteinosis

Sandeep Nayar, Manish Garg, Sunny Kalra, Amir Nadeem

Keywords : Biopsy, Breathlessness, Contrast-enhanced computerized tomography, High-resolution computed tomography, Lipoproteinaceous, Pulmonary alveolar proteinosis, Whole lung lavage

Citation Information : Nayar S, Garg M, Kalra S, Nadeem A. Unilateral Presentation of Pulmonary Alveolar Proteinosis. Indian J Chest Dis Allied Sci 2022; 64 (2):111-113.

DOI: 10.5005/jp-journals-11007-0017

License: CC BY-NC 4.0

Published Online: 08-07-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Pulmonary alveolar proteinosis (PAP) is a rare disorder, in which lipoproteinaceous material accumulates within the alveoli. We report a case of a 27-year-old male patient with acute worsening of breathlessness over the last 7–8 months and cough with desaturation up to 79% on room air. Contrast-enhanced computerized tomography of the thorax revealed unilateral diffuse crazy-paving pattern likely PAP. Transbronchial lung biopsy confirmed the diagnosis of PAP. The present case highlights the unusual presentation of PAP with unilateral involvement. To the best of our knowledge, this is the first reported case of unilateral PAP from India with a biopsy diagnosis and resolution with whole lung lavage.

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